Two Epileptic Death Cases with Postmortem Diagnosis: Tuberosclerosis Complex

  • Hüseyin Çetin Ketenci Adli Tıp Kurumu Trabzon Adli Tıp Grup Başkanlığı
  • Emel Çakır Karadeniz Teknik Üniversitesi Tıp Fakültesi Tıbbi Patoloji Anabilim Dalı
  • İbrahim Demir Adli Tıp Kurumu Trabzon Adli Tıp Grup Başkanlığı
  • Nazım Ercüment Beyhun Karadeniz Teknik Üniversitesi Tıp Fakültesi Halk Sağlığı Anabilim Dalı
Keywords: tuberous sclerosis, autopsy, epilepsy, forensic medicine, forensic pathology

Abstract

Tuberous sclerosis complex is an autosomal dominant disorder characterized by skin manifestations and formation of multiple benign tumors in different organs such as brain, kidneys, heart, liver, eyes and lungs. Two 15 years old females who had epilepsy for a long time were diagnosed TSC by autopsy performed in Forensic Medicine Institute. In this study, we aim that emphasize the importance of ‘medical autopsy’ to diagnose TSC and discuss this rare disorder which have only epilepsy in patient’s medical history in forensic medicine practice via current literature.

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Published
2017-12-23
How to Cite
1.
Ketenci H, Çakır E, Demir İbrahim, Beyhun N. Two Epileptic Death Cases with Postmortem Diagnosis: Tuberosclerosis Complex [Internet]. The Bulletin of Legal Medicine [Internet]. 23Dec.2017 [cited 19Jan.2018];22(3):218-23. doi:https://doi.org/10.17986/blm.2017228062
Section
Case Reports